Pesg PNH diagnosis, follow-up and treatment guidelines

ŞAHİN F., Akay O. M., Ayer M., Dal M. S., Ertop S., İLHAN O., ...Daha Fazla

AMERICAN JOURNAL OF BLOOD RESEARCH, cilt.6, sa.2, ss.19-27, 2016 (ESCI) identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 6 Sayı: 2
  • Basım Tarihi: 2016
  • Dergi Adı: AMERICAN JOURNAL OF BLOOD RESEARCH
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), EMBASE
  • Sayfa Sayıları: ss.19-27
  • Anahtar Kelimeler: PNH, guideline, diagnosis, treatment, PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA, COMPLEMENT INHIBITOR ECULIZUMAB, STEM-CELL TRANSPLANTATION, CLINICAL MANAGEMENT, NATURAL-HISTORY, THROMBOEMBOLISM, PREVALENCE, THROMBOSIS, PREGNANCY, DISEASE
  • Erciyes Üniversitesi Adresli: Evet

Özet

PNH Education and Study Group ( PESG) have been established in December 2013 as a non-profit, independent, medical organization www.pesg.org. Paroxysmal Nocturnal Hemoglobinuria ( PNH) is a multi-systemic disease that should be treated with a multidisciplinary approach. Patients may apply to the clinics other than the hematology due to variability and diversity of clinical findings which lower the rate of diagnosis due to low awareness about PNH. PNH might be overlooked and diagnosis might be delayed. Regarding these, PESG was established with the collaboration of Immunology, Cardiology, Thorax Diseases ( Pulmonology), Neurology, Gastroenterology, General Surgery and Urology specialists in addition to hematologists dealing with PNH. The PESG study group aims to increase the awareness about PNH, including training activities about PNH, strengthening the relations between clinics and planning of clinical studies as a goal. It is the first professional organization focusing on PNH, in Turkey. In this guideline, we want to facilitate the diagnosis attributes of physicians from all specializations that deal with PNH and its systemic complications. One can perceive this as a tailor made guideline of international guidelines but not a compilation.