Evaluation of the current disease severity scores in paediatric FMF: is it necessary to develop a new one?

KALKAN G., DEMIRKAYA E., ACIKEL C. H., POLAT A., PERU H., KARAOGLU A., ...More

RHEUMATOLOGY, vol.51, no.4, pp.743-748, 2012 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 51 Issue: 4
  • Publication Date: 2012
  • Doi Number: 10.1093/rheumatology/ker421
  • Journal Name: RHEUMATOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.743-748
  • Keywords: familial Mediterranean fever, children, outcome measurement, disease severity assessment
  • Erciyes University Affiliated: Yes

Abstract

Objectives. Modified adult disease severity scoring systems are being used for childhood FMF. We aim to test the clinical consistency of two common severity scoring systems and to evaluate the correlation of scores with the type of FMF mutations in paediatric FMF patients since certain mutations are prone to severe disease.