Deep Sedation in Difficult Airway Patient: Case Report about Dental Treatment of Hurler Scheie Syndrome (MPS IH/IS) Patient

ORBAY YAŞLI S., GÜNAY CANPOLAT D.

Eurasian Journal of Medicine and Oncology, cilt.3, ss.227-230, 2019 (ESCI) identifier

  • Yayın Türü: Makale / Vaka Takdimi
  • Cilt numarası: 3
  • Basım Tarihi: 2019
  • Doi Numarası: 10.14744/ejmo.2019.40823
  • Dergi Adı: Eurasian Journal of Medicine and Oncology
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.227-230
  • Anahtar Kelimeler: Deep sedation, dental treatment, difficult airway, hurler scheie syndrome
  • Erciyes Üniversitesi Adresli: Evet

Özet

There are a wide range of special care patients in dentistry anesthesia. As a consequence of this condition, rare syndrome are encountered. Hurler-Scheie syndrome is an inherited disorder of mucopolysaccharide metabolism, which is caused by a defect in genetically controlled pathways of lysosomal degradation. As a result, mucopolysaccharide accumulation occurs in various tissues and organs. Structural and functional deficits resulting from Hurler-Scheie Syndrome can lead to difficulties in providing safe airway, especially during anesthetic applications. There is limited data on the literature about the deep sedation practice in patients with Hurler-Scheie syndrome. We aimed to describe our experience of deep sedation for dental treatment in a child with Hurler-Scheie syndrome.